Does Usher syndrome always result in blindness?
Very few people with Usher syndrome will become totally blind – that is, have no light awareness.
Most children will be night blind but will keep their normal vision for reading and seeing fine detail so long as good lighting is available. Loss of visual field is also common, which means someone’s ability to see around them (rather than straight ahead). This causes problems for people in moving around safely, especially in unfamiliar places. Sometimes children with Usher appear to be clumsy because they trip over obstacles on the ground that they cannot see. Many people with Usher syndrome will also find it difficult to judge depth, or to see monotones (such as grey, white and black), and find that they are easily dazzled by bright light.